Epithelioid hemangioendothelioma

Abstract

Epithelioid Hemangioendothelioma (EH) is a rare, vasoformative
vascular tumour, which displays intermediate clinical behaviour between
that of hemangioma and angiosarcoma. We report a case of EH in a
30-year old female, with recurrent pericardial effusion, cough, shortness
of breath, haemoptysis, and a negative malignancy workup of pericardial
fluid aspiration cytology, and pericardial biopsy. The diagnosis of
EH was established after open lung biopsy. Our patient had a malignant
form of the disease, who had evidence of alveolar haemorrhage terminally. This is the first case being reported from Nepal. Chemotherapy was
advised which she refused, and she died within five months of onset of symptoms.